Kalıtsal Kanama Bozukluklarında Kanıta Dayalı Fizyoterapi Yaklaşımları

Kalıtsal kanama bozuklukları kandaki pıhtılaşma faktörleri eksikliğinden kaynaklanan nadir hastalıklardır. Hemofili A, Hemofili B ve von Willebrand hastalığı prevelansı en fazla olan kanama bozukluklarıdır. Kalıtsal kanama bozukluklarında en sık kas-iskelet sistemi kanamaları gözlenmektedir. Tekrarlayan bu kanamalar eklemde dejenerasyonlara neden olabilmektedir. Muhtemel kanamaların önlenmesi ve hemofilik artropati semptomlarının iyileştirilmesi amacıyla çeşitli fizyoterapi yöntemleri kullanılmaktadır. Bu derlemenin amacı kalıtsal kanama bozukluklarında kanıta dayalı fizyoterapi yaklaşımları hakkında bilgilendirme sağlamaktır.

Anahtar Kelimeler:

Fizik tedavi, hemofili, kan pıhtılaşma bozuklukları, rehabilitasyon

Evidence-Based Physiotherapy Approaches in Congenital Bleeding Disorders

Inherited bleeding disorders are rare diseases caused by low levels of clotting factors in the blood. Hemophilia A, Hemophilia B, and von Willebrand disease are the bleeding disorders with the highest prevalence. Musculoskeletal bleeding is the most common in hereditary bleeding disorders. These recurrent bleedings can cause degenerations in the joint. Various physiotherapy methods are used to prevent possible bleeding and to relief the symptoms of hemophilic arthropathy. The aim of this review is to provide information about evidence-based physiotherapy approaches in hereditary bleeding disorders

Keywords:

Physical therapy, hemophilia, blood coagulation disorders, rehabilitation,

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