Tuba BAYINDIR, Yüksel KABLAN, Mehmet T ÇİÇEK, Tamer ERDEM

Melkersson Rosenthal Sendromu: İki Olgu

Melkersson Rosenthal Sendromu, tekrarlayan fasiyal paralizi, ağrısız ve gode bırakmayan orofasiyal ödem, fissürlü dil triadı ile karakterize, etiyolojisi net olarak bilinmeyen ve nadir görülen bir hastalıktır. Klasik triadın görülmesi nadirdir, genellikle tek ya da iki semptom birlikte görülür. Bu sunumda, öykü ve klinik özellikleri ile Melkersson Rosenthal Sendromu tanısı konan iki olgu tartışılacaktır. Otuzbir yaşında bir erkek hastada ve 16 yaşında bir kız hastada öykü ve klinik özellikleri ile Melkersson Rosenthal Sendromu'nun tanısı konulmuştur. Hastaların her ikisi de 1 mg/kg/gün oral prednizolon ile tedavi edilmiştir. Tekrarlayan fasiyal paralizi olgularında Melkersson Rosenthal Sendromu düşünülmelidir.

Melkersson Rosenthal Syndrome: Report of Two Cases

Melkersson-Rosenthal Syndrome is a rare disease of unknown etiology, being characterized by the triad of recurrent facial nerve palsy, gode-free orofacial edema and fissured tongue. Classical triad of this syndrome is rarely present, especially single or two symptoms can be seen. In this report, two cases who diagnosed as Melkersson Rosenthal Syndrome according to the history and clinical features will be discussed. Melkersson Rosenthal Syndrome was diagnosed in two patients; thirty-one year old male and 16 year old girl patient, according to the history and clinical features. Both of them were treated with 1 mg/kg/day oral prednisolone. We will discuss two cases, which were diagnosed as Melkersson-Rosenthal Syndrome with history and clinical features.

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