Şenol ADANUR, Ercüment KESKİN, Elif DEMİRCİ, Tevfik ZİYPAK, Turgut YAPANOĞLU, İsa ÖZBEY

Prımary Renal Malignant Fibrous Histiocytoma

Malign fibröz histiyostom, adultlarda retroperitonum ve ekstremitelerde oluşan en yaygın yumuşak doku sarkomudur. Ancak böbreğin primer malign fibröz histiyositomu oldukça nadirdir. Malign fibröz histiyositomun klinik ve histopatolojik tanısı ürologlar ve patologların her ikisi içinde zorluklar oluşturur. Burada histopatolojik ve klinik tanısının yanısıra, klinik ve radyolojik prognozunu tartışarak bu nadir görülen leyzonu sunmayı amaçladık

Anahtar Kelimeler:

Malign fibröz histiyositom, böbrek, tedavi

Prımary Renal Malignant Fibrous Histiocytoma

Malignant fibrous histiocytoma (MFH) is the most common soft tissue sarcoma in adults occurring in the extremities and retroperitoneum. However, primary MHF of the kidney is extremely rare. Clinical, and histopathological diagnosis of MFH creates difficulties both for urologists, and pathologists. Herein, we aim to present this rarely seen lesion, and discuss its clinical, and radiological prognosis, as well as its histopathological and clinical diagnosis.

Keywords:

Malignant fibrous histiocytoma, kidney, treatment,

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Papadopoulos I, Rudolph P. Primary renal malignant fi- brous histiocytoma: case report. Urol Int 1999; 63:136–8
Ozello L, Stout AP, Murray MR. Cultural characteristics of malignant histiocytomas and fibrous xanthomas. Cancer 1963;16: 331
Tarzan M, Cserni G, Szabo Z. Malignant Fibrous Histiocytoma of the kidney. Scand J Urol Nephrol 2001;35:518–20
Ptochos A, Karydas G, Iosifidis N, et al. Primary renal malignant fibrous histiocytoma: a case report and review of literature. Urol Int 1999; 63:261–7
Sierra Labarta R, Gil Sanz MJ, Muñoz González G, Rioja Sanz LA. A new case of malignant fibrous histiocytoma aris- ing from the renal capsule. Actas Urol Esp 2010;34:122-4
Weiss SW, Goldblum JR (eds). Malignant fibrohistiocytic tumors. In: Enzinger and Weiss’s Soft Tissue Tumors. 4th edn. Mosby, St Louis 2001; 535–70
SS Hwang, SY Park and YH Park. The CT and 18F-FDG PET/ CT appearance of primary renal malignant fibrous histio- cytoma. J Med Imaging Radiat Oncol 2010;54:365–7
Takashi M, Murase T, Kato K, Koshikawa T, Mitsuya H. Malignant fibrous histiocytoma arising from the renal capsule: report of a case. Urol Int 1987; 42:227-30
Froehner M, Manseck A, Haase M, Hakenberg OW, Wirth MP. Locally recurrent malignant fibrous histiocytoma: a rare and aggressive genitourinary malignancy. Urol Int 1999;62: 164-70