Hakan ALTIN, Hayrullah ALP, Fatih ŞAP, Zehra KARATAŞ, Tamer BAYSAL, Sevim KARAASLAN

Double Aortic Arch with Mirror-image Dextrocardia

Çift arkus aorta (ÇAA) nadir bir konjenital vasküler anomali olup, beslenme ve/veya solunum problemleri ile sonuçlanan, trakea ve özefagusun çevrelenmesi ile karakterizedir. Bu makalede, situs inversus totalis ile birlikte ÇAA bulunan 2 aylık bir kız hasta sunulmuştur. Bebeğin doğumdan beri sesli soluk alma ve öksürük semptomları bulunmaktaydı. Çift arkus aorta, ekokardiagrafi, baryumlu özofagografi, kardiak MR ve konvensiyonel anjiografi ile saptandı. Bu makalede, solunum ve/veya beslenme problemleri olan bir hastada vasküler halkanın mutlaka araştırılması gerektiği vurgulanmıştır. Göğüs grafisi, baryum özofagografi, ekokardiografi, multislice bilgisayarlı tomografi, magnetic rezonans görüntüleme anjiografi ve konvansiyonel kardiyovasküler anjiografi ÇAA tanısında kullanılabilir

Anahtar Kelimeler:

Çift arkus aorta, dekstrokardi, vasküler halka

Double Aortic Arch with Mirror-image Dextrocardia

Double aortic arch (DAA) is a very rare congenital vascular anomaly, characterized by the encircling trachea and esophagus, resulting feeding and/or respiratory problems. In this article, a two-month-old girl with situs inversus totalis and DAA was presented. The baby was symptomatic with noisy breathing and coughing since birth. Double aortic arch was detected by echocardiography, barium esophagography, cardiac MRI and conventional angiography. The present report emphasis that vascular ring should have been evaluated in a patient with respiratory and/or feeding problems. Chest radiography, barium esophagography, echocardiography, multislice computed tomography, magnetic resonance imaging angiography and conventional cardiovascular angiography can be used for the diagnosis of DAA.

Keywords:

Double aortic arch, dextrocardia, vascular ring,

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