Corresponding Author: Roopesh Sankaran MD, Department of Otorhinolaryngology and Head and Neck Surgery, Faculty of Medicine

This is case where an elderly woman referred to our clinic with history of recurrent epistaxis from right nostril for one year duration associated with persistent right nasal blockage, hyposmia, loss of weight and loss of appetite. On examination noted polypoidal mass at right sphenoethmoidal recess with evidence of previous surgery. Patient underwent endoscopic removal of the mass and histopathologic examination was reported as malignant small round blue cells tumors from right olfactory cleft and right ethmoidal air cells. Based on immunohistochemical examination, it was consistent with primitive neuroectodermal tumour (PNET).

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1. Batsakis JG, Mackay B, el-Naggar AK. Ewing's sarcoma and peripheral primitive neuroectodermal tumor: an interim report. Ann Otol Rhinol Laryngol 1996; 105: 838-843.

2. Patil AM, Yendigeri SM, sajjanar BB, Kudadi SS. Ewing sarcoma/ PNET of sinonasal region: a rare case report. www.sciencejournal.in. 2013; 2(2).

3. Stout AP. A tumor of the ulnar nerve. Proc NY Pat Soc 1918; 18: 2-11.

4. Heung ML, Seung HH, Jeong SW, et al. Primitive neuroectodermal tumor of nasal cavity: case report. J Rhinol. 1997; 4: 57-60.

5. Jurgens H, Bier V, Harma D, et al. Malignant peripheral neuroectodermal tumors: a retrospective analysis of 42 patients. Cancer 1988; 61: 349-357.

6. Chowdhury K, Manoukian JJ, Rochon L, Begin LR. Extracranial primitive neuroectodermal tumor of the head and neck. Arch Oto- laryngol Head Neck Surg 1990; 116: 475-478.

7. Iezzoni JC, Mills SE. "Undifferentiated" small round cell tumors of the sinonasal tract: Differential diagnosis update. Am J clin Pathol 2005; 124: 110- 121.

8. Carvajal R, Meyer P. Ewing's sarcoma and primitive neuroectodermal family of tumor. Hematol Oncol Clin North Am. June 2005; 19: 501-525.

9. Jones JE, McGill T. Peripheral primitive neuroectodermal tumors of the head and neck. Arch Otolaryngol Head Neck Surg 1995; 121: 1392- 1395.

10. Kushner BH, Haydu S, Gulati SC. Extracranial primitive neur- oectodermal tumors. Cancer 1991; 67: 1825-1826.