Ülviye YALÇINKAYA, Hakan TURAN, Semra TOKER, Hayriye SARICAOĞLU

A Case Of Linear Scleroderma Following Blaschko's Lines

Lineer skleroderma lokalize sklerodermanın nadir bir varyantıdır, tipik olarak çocuklarda görülür ve ekstremite yerleşimlidir. 21 yaşında bayan hastanın gövdesinin sağ üst yarısında meme üzerinden başlayıp ark çizerek sağ kola uzanan ve sonra lineer devam eden belirgin sınırlı, hiperpigmente, sklerotik bir plağı vardı ve antinükleer antikoru pozitifti. Histopatolojisi skleroderma ile uyumlu idi. Hastaya lineer skleroderma tanısı konuldu. Lokalize sklerodermanın Blaşko çizgisini takip edip etmediği tartışmalı bir konudur. Bu vakayı sunmakla lokalize sklerodermanın Blaşko çizgilerini takip edebileceğini düşünerek literatüre katkıda bulunmayı amaçladık.

Blaşko Çizgisini Takip Eden Lineer Sklerodermalı Bir Vaka

Linear scleroderma is a rare variant of localized scleroderma typically seen in children and localized in the extremities. A 21-year-old female patient had a well-defined, hyper-pigmented, sclerotic plaque on right half of the frontal trunk, starting from the breast and arcing up to the right arm, then continuing linearly with anti-nuclear antibody positivity in her laboratory results. Histopathology was compatible with scleroderma. She was diagnosed linear scleroderma. There is an ongoing argument on whether localized scleroderma follows Blaschko s lines or not. By presenting this case, we aimed to contribute to literature claiming that localized scleroderma may follow Blaschko s lines.

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