MEHMET AKDAĞ, Fazıl Emre ÖZKURT, Beyhan YILMAZ, İsmail TOPÇU, Faruk MERİÇ

Bilateral ve tekrarlayan fasiyal paralizinin nadir nedeni: Melkersson-Rosenthal sendromu

Melkersson-Rosenthal Sendromu yineleyen periferik fasiyal paralizi, orofasiyal ödem ve fissürlü dil triadı ile karakterize granülomatöz hastalıktır. Bu yazımızda çocukluktan itibaren 2 kez sol ve bir kez sağ taraftan periferik paralizi atağı geçiren ve idiopatik fasiyal paralizi tanısı alan olgunın kliniğimize tekrar sağ tarafta periferik fasiyal paralizi ön tanısı ile yatırılıp tetkik ve takip sonucunda Melkersson-Rosenthal Sendromu (MRS) tanısı alan hastada; fasiyal paralizinin farklı tarafta ve farklı zamanlarda tekrarlayıcı olması ve tedaviye dirençli olması ve ayrıca gençlik çağında ender görülüyor olması nedeniyle sunulmuştur. Ancak bu sendromla ilgili gerek doğru etiyoloji ve gerekse sonuç veren tedavi açısından klinikopatolojik ek çalışmalara ihtiyaç duyulmaktadır.

A rare cause of bilateral and recurrent facial palsy: Melkersson-Rosenthal sendromu

Melkersson-Rosenthal syndrome is a granulomatous disease which is characterized by the triad of recurrent peripheral facial palsy, orofacial edema, and fssured tongue. In this article we presented one case who, since childhood, had had peripheral paralysis attack twice on the left side and once in the right side and was diagnosed with idiopathic paralysis before being admitted to our clinic for the second time with the preliminary diagnosis of peripheral facial paralysis on the right side and then diagnosed and followed up with the diagnosis of Melkers - son-Rosenthal Syndrome (MRS). We presented this case since the facial paralysis recurred on the different side and in different times and also since it remained resistant to treatment of steroids and it is seen rarely in adolescence. However, further clinic-pathological studies are required to investigate the etiology and fnd right treatment

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