OSTEOGENEZİS İMPERFEKTA HASTASININ DİŞ TEDAVİSİ: BİR OLGU SUNUMU

Osteogenezis İmperfekta ’kırılgan kemik hastalığı’ kemik kırılganlığında artma ve iskeletsel deformiteler ile ilişkilendirilmektedir. Bu hastalarda aile öyküsü, mavi sklera, duyma kaybı, dentinogenezis imperfekta gibi belirgin klinik özellikler gözlenebilmektedir. Bu vakada Kahramanmaraş Sütçü İmam Üniversitesi Çocuk Diş Hekimliği Bölümü’nde tedavi edilen 11 yaşındaki Osteogenezis İmperfekta’lı kız hasta sunulmaktadır. Hastanın yüzünde asimetri ve üçgensel form, boy kısalığı, pektus ekskavatum veya karinatum gibi göğüs duvarında ve ayaklarında deformiteler tespit edilmiştir. Hastanın klinik ve radyografik muayenesi sonucunda çürük dişlerine dolgu uygulamıştır. Hastamız çocuk diş hekimliği ve ortodonti bölümünde düzenli aralıklarla kontrol altındadır. Anahtar Kelimeler: Osteogenezis İmperfekta, çocuk, diş tedavisi ABSTRACT Osteogenesis Imperfecta ‘brittle bone disorder’ is associated with bone fragility and skeletal deformities. Significant clinical features such as family history, blue sclera, hearing loss, dentinogenesis imperfecta may be observed in these patient. This article reports a case of Osteogenesis Imperfecta in a eleven-year-old female patient treated in Kahramanmaraş Sütçü Imam University, Department of Pediatric Dentistry. Asymmetry and triangular form of the patient’s face, short stature, pectus excavatum or carinatum deformities on chest wall and feet were detected. The clinic signs and symptoms of the patient were detected and the treatment plan was analyzed. In routine clinic dental examination and filling and protective applications were successfully applied. The patient is still under regular control by pediatric and orthodontic department. Key Words: Osteogenesis Imperfekta, child, dental treatment

Anahtar Kelimeler:

Osteogenezis İmperfekta, çocuk, diş tedavisi

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