Murat UÇAR, İrfan KIRIŞTIOĞLU, Nizamettin KILIÇ, Fatih ÇELİK, Ahsen Karagözlü AKGÜL

Complete Penile Duplication with Structurally Normal Penises: A Case Report

Background: Diphallia is a very rare anomaly and seen once in every5.5 million live births. True diphallia with normal penile structures isextremely rare. Surgical management for patients with complete penileduplication without any penile or urethral pathology is challenging.Case Report: A 4-year-old boy presented with diphallia. Initialphysical examination revealed first physical examination revealedcomplete penile duplication, urine flow from both penises, meconiumflow from right urethra, and anal atresia. Further evaluations showeddouble colon and rectum, double bladder, and large recto-vesicalfistula. Two cavernous bodies and one spongious body were detectedin each penile body. Surgical treatment plan consisted of right totalpenectomy and end-to-side urethra-urethrostomy. No postoperativecomplications and no voiding dysfunction were detected during the18 months follow-up.Conclusion: Penile duplication is a rare anomaly, which presentsdifferently in each patient. Because of this, the treatment shouldbe individualized and end-to-side urethra-urethrostomy may be analternative to removing posterior urethra. This approach eliminatesthe risk of damaging prostate gland and sphincter.

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