Ayca Pinar Nas, Yasemin MEN ATMACA, Oksan DERİNOZ GULERYUZ

Systemic steroid treatment of rarely seen genitourinary system manifestation in children with Henoch Schönlein purpura: Case report and literature analysis

Henoch-Schönlein Purpura (HSP) is the most commonly seen systemic leukocytoclastic vasculitis in children. Although it frequently presents with skin, joint, and gastrointestinal system involvement, genitourinary system involvement is rarely seen as well. We present a child with HSP-associated penile and scrotum involvement and a literature review was performed. An eight-years-oldmale patient who underwent five days systemic, five days oral steroid therapy in hospital and had a total recovery from the HSPassociated penile and scrotum involvement that is rarely reported in the literature. Scrotum and penile involvement are rare in patients with HSP; acceptable with a good prognosis. Disease-related genitourinary system involvement may be associated with findings such as penis and scrotum involvement, balanitis, urethritis, hematoma in the bladder wall, epididymo-orchitis and priapism. In the literature, most commonly scrotal edema or only penile involvement is mentioned. However, treatment for HSP is controversial,steroid and analgesic treatment can be applied in patients with HSP and penile/scrotum involvement.

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