Huntington koresinde anestezik yaklaşım (olgu sunumu)

Huntington koresi nadir görülen ve bazal ganglionlarda atrofi ile karakterize, genetik olarak otozornal dominant geçiş özelliğine sahip bir santral sinir sistemi hastalığıdır. Başlıca klinik bulgular; köre, ataksi, dizartri ve progresif demanstır. Bu hastalarda anestezi uygulaması sırasında karşılaşılan önemli sorunlar; koreoatetoid hareketler, kooperasyon güçlüğü, anestezik ilaçlara olağan dışı yanıtlar ve pulmoner aspirasyon riskidir. Bu çalışmada, ortopedik operasyon geçiren Huntington kareli bir hastada droperidol, remifentanil ve atrakuryıım ile modifiye nörolept anestezinin uygulandığı anestezik yaklaşım sunuldu.

Anahtar Kelimeler:

Huntington hastalığı, Anestezi, Erişkin, Tedavi sonucu, Risk faktörleri, Nörolept analjezi, Erkek

Anesthetic approach in Huntington's chorea

Huntington's chorea, transmitted in an autosomal dominant pattern, is a genetically determined rare disease of the nervous system. There is degeneration with atrophy in the basal ganglia. The main clinical signs are chorea, ataxia, dysarthria and progressive dementia. In these patients, the potential important problems during anesthetic practice are choreoatetoid movement, abnormal response to anesthetic agents, difficult cooperation and risk of pulmonary aspiration. In this study, anesthetic approach to a patient with Huntington's chorea undergoing orthopedic operation performed with a modified neuroleptanesthesia including droperidol, remifentanil and atracurium was presented.

Keywords:

Huntington Disease, Anesthesia, Adult, Treatment Outcome, Risk Factors, Neuroleptanalgesia, Male,

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