Yeliz Dadalı, İlke Bursalı, Sercan Özkaçmaz, Mustafa Demir

2000 Hastada Konjenital Mediastinal Vasküler Anomali Tiplerinin ve Sıklığının Değerlendirilmesi

Amaç: Bu çalışmamızda bölgemizde konjenital mediastinal vasküler anomalilerin sıklığını araştırmayı planladık. Yöntem: Yaklaşık 2 yıllık bir süreçte non-spesifik semptomlar ile kontrastlı toraks Bilgisayarlı Tomografi çekilen hastaların özellikleri hastane veri tabanından retrospektif olarak tarandı. Yaş ve cinsiyet gibi demografik özellikler kaydedildi. Tüm Bilgisayarlı Tomografi görüntüleri, persistan sol superior vena kava, azygos lobu, aberran sağ subklavien arter, dilate sol superior interkostal ven, sağ taraflı arkus aorta, situs inversus ve parsiyel anormal pulmoner venöz dönüş anomalileri açısından yorumlandı. Çalışmamızda bulunan insidans değerleri ile önceki çalışmaların sonuçları karşılaştırıldı. Bulgular: Mediastinal vasküler anomali 62 (%3.1) hastada saptandı. Kadın hastaların 27 (%3.5)’inde ve erkek hastaların 35 (%2.6) ’inde bir mediastinal vasküler anomali gözlemlendi. Çalışmamızdaki en sık saptanan mediastinal vasküler anomali, sağ aberran subklavien arter (n:17, %0.9) ve en nadir görüleni ise parsiyel anormal pulmoner venöz dönüş anomalisi idi (n:1, %0.1). Persistan sol superior vena kava insidansı %0.3 (n:6), azygos lobu %0.7 (n:14), sağ taraflı arkus aorta %0.3 (n:5), situs inversus totalis %0.2 (n:3) ve genişlemiş sol superior interkostal ven ise %0.8 (n:16) olarak bulundu. Sonuç: Mediastinal vasküler anomaliler nadir olup sıklıkla asemptomatiktir. Ancak bu durumların görüntüleme bulgularının iyi bilinmesi, girişimsel işlemleri doğru biçimde planlamada ve aynı zamanda iatrojenik yaralanmaları önlemede gereklidir.

Evaluation of Congenital Mediastinal Vascular Anomaly Types and Frequencies Among 2000 Cases.

Aim: In this study, it was aimed to examine the incidence of congenital thoracic vascular anomalies in our region. Methods: The features of the patients with non-specific complaints who underwent a thorax Computed Tomography over a two years period were retrospectively reviewed on the hospital database, and demographical data (Gender and age) were recorded. All the Computed Tomography images were interpreted regarding thoracic vascular anomalies, including persistent left superior vena cava, azygos lobe, aberrant right subclavian artery, dilated left superior intercostal vein, right-sided aortic arch, situs inversus, and partial anomalous pulmonary venous return. The incidences of these thoracic vascular anomalies were calculated and compared with previous studies. Results: Mediastinal vascular anomaly was detected in 62 (3.1%) patients. A mediastinal vascular anomaly was observed in 27 (3.5%) female patients and 35 (2.6%) male patients. The most common mediastinal vascular anomaly in this study was the right aberrant subclavian artery (n:17, 0.9%) and the rarest was partial anomalous pulmonary venous return (n:1, 0.1%). Persistent left superior vena cava incidence was 0.3% (n:6), azygos lobe 0.7% (n:14), right-sided aortic arch 0.3% (n:5), situs inversus totalis 0.2% (n:3), and dilated left superior intercostal vein 0.8% (n:16). Conclusion: Mediastinal vascular anomalies are rare and usually asymptomatic. But the imaging findings of these conditions must be well-known to accurately planning the interventions and also to prevent iatrogenic injuries.

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