Üç yaşındaki erkek çocukta mesane rabdomyosarkomu: Olgu sunumu
Rabdomyosarkom, çocukluk çağında alt üriner sistemin en sık görülen malign tümörüdür. Başvuru semptomları arasında hematüri, abdominal veya pelvik kitle, idrar yaparken zorlanma gibi infrevezikal obstrüktif yakınmalar ile üriner inkontinans ve üriner sistem enfeksiyonları saptanabilmektedir. Bu makalede, mesane rabdomyosarkomu saptanan 3 yaşındaki bir erkek olgunun öyküsü, klinik özellikleri, yapılan tanısal incelemeler ve tedavi seçenekleri sunularak literatür eşliğinde tartışılmıştır.
Bladder rhabdomyosarcoma in a 3 year old boy: Case report
Rhabomyosacroma is the most frequently seen malignant tumor of the lower urinary tract in children. Hematuria, abdominal or pelvic mass, infravesical obstructive symptoms such as difficulty in voiding, urinary incontinence and urinary tract infections are the most commonly seen admitting symptoms. In this paper, a 3 year old boy with the diagnosis of bladder rhabdomyosarcoma is presented and discussed including history, clinical findings, diagnostic work-up and treatment alternatives.
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- 1.Ferrer FA, Isakoff M, Koyle MA. Bladder/Prostate Rhabdomyosarcoma: Past, Present and Future. J Urol 2006; 176: 1283-1291.
- 2.Raney B, Anderson J, Jenney M, et al. Late effects in 164 patients with rhabdomyosarcoma of the bladder/prostate region: A report from the international workshop. J Urol 2006; 176: 2190-95.
- 3.Wu Hy, Snyder HM. Pediatric urologic oncology; bladder, prostate, testis. Urol Clin N Am 2004; 31: 619-627.
- 4.Flamant F, Rodary C, Rey A et al. Treatment of rhabdomyosarcoma in childhood and adolescence. Results of the second International Society of Paediatric Oncology MMT84. Eur J Cancer 1998; 34: 1050-62.
- 5.Raney RB Jr, Gehan EA, Hays DM et al. Primary chemotherapy with or without radiation therapy and/or surgery for children with localised sarcoma of the bladder, prostate, vagina, uterus and cervix. A comparison of the results of Intergroup Rhabdomyosarcoma I and II. Cancer 1990; 66: 2072-81.
- 6.El-Sherbiny MT, El-Mekresh MH, El-Baz MA, et al. Paediatric lower urinary tract rhabdomyosarcoma: a single-centre experience of 30 patients. BJU Int 2000; 86: 260-7.
- 7.Arndt C, Rodeberg D, Breitfeld PP, et al. Does bladder preservation (as a surgical principle) lead to retaining bladder function in bladder/prostate rhabdomyosarcoma? Results from Intergroup Rhabdomyosarcoma Study-IV. J Urol 2004; 171: 2396-403.