Ergun ALMA, Hakan ERÇİL, Mehmet Eflatun DENİZ, Ferhat ORTOĞLU, Orçun ÇELİK, Zafer Gökhan GÜRBÜZ

Fonksiyonel mesane paraganglioması: Olgu sunumu

İlk olarak 1953 yılında Zimmerman tarafından tanımlanan extraadrenal feokromasitomalar, paraganglioma olarak isimlendirilir. Genito üriner paraganglioma, tüm paragangliomaların %1’inden azını oluşturmaktadır. Üriner sistemde en sık olarak etkilenen organ mesanedir. Daha az sıklıkla renal pelvis ve üreter etkilenmektedir. Sıklıkla 20-40 yaş arası kadınlarda izlenmektedir. Hastaların semptomları tümörün salgıladığı katekolaminler ile ilişkilidir ve en sık hipertansiyon, baş ağrısı, hematüri ve senkop/palpitasyondur. Biz bu vaka sunumumuzda 56 yaşındaki erkek hastada saptadığımız mesane paragangliomasının tedavisini literatür eşliğinde tartışmayı amaçladık.

Anahtar Kelimeler:

Paraganglioma, me- sane, cerrahi tedavi

Functional paraganglioma of bladder: A case report

Extraadrenal phoechromacytomas are also called paragangliomas that were firstly described by Zimmerman at 1953. Less than 1% of all paragangliomas are genitourinary paragangliomas. Bladder is the most affected organ in the urinary system also renal pelvis and ureter was less affected than bladder too. It was frequently occured 20-40 years age women population.The symptoms of patients are related to cathecolamins that was secreted by tumour and the most of symptoms are hypertension, headache, hematuria and syncope/palpitation. In our case presentation, we aimed to discuss treatment of bladder paraganglioma that occured in 56 years age male patient with current literature.

Keywords:

Paraganglioma, bladder, sur- gical treatment,

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