Tuberosklerozlu bir olguda kardiyak rabdomyom: 5 yıllık izlemde tümörün kendiliğinden kaybolması

Rabdomyom çocuklarda en sık görülen kardiyak tümör olup genellikle tuberoskleroz ile birliktedir. Çoğunluğu benign seyirlidir ve kendiliğinden gerilemektedir. Kiniği-mize üfürüm değerlendirilmesi amacıyla yönlendirilen ve kardiyak rabdomyom tanısı alan, bir yaşında tuberoskle-rozu da tespit edilen ve 5 yıllık izlem sonunda tümörü tamamıyla kaybolan beş aylık erkek hasta sunuldu.

Anahtar Kelimeler:

Rabdomiyom, Süt çocuğu, Erkek, Tüberoskleroz, Ekokardiyografi

Cardiac rhabdomyoma in a patient with tuberous sclerosis: Spontaneous regression in a 5-year follow-up

Rhabdomyoma is the most common cardiac tumor in children usually associated with tuberous sclerosis. Rhabdomyoma has mostly a benign course and regresses spontaneously. In this report, a case of cardiac rhabdomyoma associated with tuberous sclerosis in a five months old male patient referred to our clinic for evaluation of cardiac murmur is presented. After a 5 year-follow up, the tumor completely resolved spontaneously.

Keywords:

Rhabdomyoma, Infant, Male, Tuberous Sclerosis, Echocardiography,

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