Seçil ARSLANSOYU ÇAMLAR, ALPER SOYLU, AYHAN ABACI, Mehmet Atilla TÜRKMEN, Ayfer ÜLGENALP, Salih KAVUKÇU

Horseshoe kidney with growth retardation: Don't forget Turner syndrome

ISSN: 0041-4301
Yayın Aralığı: Yılda 6 Sayı
Başlangıç: 1958
Yayıncı: Hacettepe Üniversitesi Çocuk Sağlığı Enstitüsü Müdürlüğü

Horseshoe kidney is the most frequent renal fusion anomaly that is usually asymptomatic and isolated malformation. However it can be seen with various syndromes and chromosomal anomalies. It was reported that 15-35% of Turner syndrome cases (TS) also display horseshoe kidney condition. TS is a chromosomal anomaly that had been characterized by delayed puberty, short body height and gonadal dysgenesis. In this report a five-year-old girl with horseshoe kidney, which has growth retardation during follow-up as only symptom of Turner syndrome.

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