Congenital aneurysm of the left atrial appendage can be caused by congenitaldysplasia of the pectinate muscles and may be accompanied by a congenitalabsence of the pericardium. Symptoms generally manifest after two decadesand the most common symptom is atrial arrhythmia in the form of atrialfibrillation / flutter. A four year-old patient with no symptoms underwentan echocardiographic examination for the investigation of a heart murmur.Echocardiographic examination revealed a large cystic lesion occupying the lefthemithorax and compressing the left ventricle. The patient was referred toour center. The lesion caused displacement of the heart rightward behind thesternum which made the examination difficult. We aimed to present this rarecase of giant left atrial appendage aneurysm in the light of current literature.
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