A pediatric case of Ortner’s syndrome caused by heritable pulmonary arterial hypertension and review of the literature

An 11-year-old male, who complained of hoarseness and fatigue on effortpresented to our institution for evaluation. Left vocal cord paralysis andsevere pulmonary hypertension was diagnosed. The patient had an enlargedpulmonary artery due to pulmonary hypertension which was responsiblefor compression to left vocal cord paralysis causing hoarseness. Ortner’ssyndrome or cardiovocal syndrome is known as hoarseness due to left vocalcord paralysis secondary to cardiac pathologies. Although hoarseness of voiceis frequently encountered in the otorhinolaryngology clinics, pulmonaryhypertension related hoarseness is an unusual presentation in childhood.

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Turkish Journal of Pediatrics-Cover
  • ISSN: 0041-4301
  • Yayın Aralığı: Yılda 6 Sayı
  • Başlangıç: 1958
  • Yayıncı: Hacettepe Üniversitesi Çocuk Sağlığı Enstitüsü Müdürlüğü
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