Bayram METİN, Mustafa Fatih ERKOÇ, Sevinç ŞAHİN, Yavuz Selim İNTEPE

Multi organ tutulumlu tüberosklerozda lenfanjiyoleiyomiyomatozise bağlı spontan tansiyon hemopnömotoraks olgusu

Tuberosklerozis kompleksi, beyin, akciğer, böbrek, göz, kalp, kemik ve deri gibi organları etkileyebilen genetik bir hastalıktır. Pulmoner lenfanjiyoleiyomiyomatozis daha çok genç erişkin bayanlarda görülen bir hastalıktır. Akciğer parankimindeki düz kas hücrelerinin neoplastik olmayan atipik proliferasyonu ile karakterizedir. Biz burada literatürde karşılaşmadığımız tuberosklerozis hastasında lenfanjiyoleiyomiyomatozise bağlı spontan hemopnömotoraks olgusunu sunuyoruz.

Anahtar Kelimeler:

tuberosklerozis, lenfanjiyoleiyomiyomatozis, hemopnömotoraks

Lymphangioleiomyomatosis-associated spontaneous tension hemopneumothorax in multiple organ involvement tuberculosis

Tuberosclerosis complex is a genetic disorder that can affect several organs (such as the brain, lungs kidneys, eyes, the heart, bones and the skin). Pulmonary lymphangioleiomyomatosis is a disease that is mostly seen among young adult women. It is characterized primarily by the non-neoplastic atypical proliferation of smooth muscle cells in the lung parenchyma. Here, we present a case of lymphangioleiomyomatosis-associated spontaneous hemopneumothorax in a tuberosclerosis patient, which we did not encounter in the literature.

Keywords:

tuberoussclerosis, lymphangioleiomyomatosis, hemopneumothorax,

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