Yenidoğan döneminde saptanan dev koroner arter fistülü

Koroner arter fistülleri, koroner arterler ile kalp boşlukları veya büyük damarlar arasında olan bağlantılar olup, nadir görülen kardiyak anomalilerdir. Her yaşta görülebilirler. Anormal üfürüm, dispne, anjina, yorgunluk, çarpıntı gibi semptomlar nedeniyle tetkik edilirken de saptanabilirler. Bu olgu sunumunda, kliniğimize üfürüm nedeniyle gönderilen ve sol ana koroner arterden kaynaklanarak sağ atriyuma açılan dev fistül saptanan dört günlük bir yenidoğan sunuldu. Bu olgu sunumu ile nadir görülmesine rağmen, üfürüm duyulan bebeklerde koroner arter fistüllerinin de ayırıcı tanıda düşünülmesi gerektiği ve ekokardiyografinin tanıdaki önemi vurgulanmak istendi.

Giant coronary artery fistula diagnosed in newborn period

Coronary artery fistulas are rare cardiac anomalies which are connections between coronary arteries and the lumen of cardiac chambers or great arteries. They can be seen in all ages. They can be diagnosed during investiagation of abnormal murmurs, dyspnea, angina, fatigue, and palpitations. In this case report, a four days old newborn is reported who was admitted to our department with heart murmur. A giant fistula originating from left main coronary artery and draining into the right atrium was diagnosed. With this case report, we wanted to emphasize the importance of echocardiography in the diagnosis of coronary artery fistulas. Although rarely observed they should be considered in the differential diagnosis of infants with murmur.

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