Vulvanın Paget Hastalığı: Olgu Sunumu

Meme dışı Paget hastalığı, kaşıntı, ağrı ve egzema gibi iyi huylu hastalıklarla ortak belirtilere sahip olan nadir bir malign neoplazidir. Vulvar hastalık, genellikle postmenopozal kadınlarda etkilenen bölge üzerinde kabuklanma veya ülserasyonlu yavaş büyüyen iyi tanımlanmış kaşıntılı bir plak olarak görülür. Bu, tanıda gecikmeye ve sonuç olarak daha kötü prognoza yol açar.Kesin tanı, Paget hücrelerini gösteren vulva biyopsisi ile elde edilir.Tercih edilen tedavi, marjinin geniş eksizyonudur. Bizim hastamız 9 ay süren benzer yakınma öyküsü olan 73 yaşında postmenopozal bir kadındır. Tanı koymak için yapılan geniş bir biyopsinin tedavi edici rolü de vardır

Paget's Disease of the Vulva: A Case Report

Extra mammary Paget disease is a rare malign neoplasm that may affect the vulva and has manifestations common to benign diseases such as itching, pain and eczema. Vulvar disease usually presents as a slow growing well-defined itchy plaque with crustations or ulcerations over the affected area in postmenopausal women. This leads to delay in diagnosis and consequent worse prognosis. The definitive diagnosis is obtained by biopsy of the vulva, which shows Paget cells. The treatment of choice is wide excision with margins. Our patient is a 73-year-old postmenopausal woman with a history of similar complaints of 9 months’ duration. A large biopsy to diagnose also has a therapeutic role

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