Ağır nefrotik sendrom ile başvuran erişkin bir hastada Henoch-Schönlein purpurası

Erişkinlerde Henoch-Schönlein Purpurası (HSP), ender görülen klinik bir tablodur. HSP nefriti sıklıkla asemptomatik idrar bulgularıyla seyretmekle birlikte, ağır nefrotik sendromla başvuru oldukça enderdir ve kötü renal sonlanımla ilişkilidir. Burada ağır nefrotik sendromla başvurup HSP nefriti tanısı alan, steroid ve siklofosfamid tedavisiyle tam remisyon sağladığımız bir olgu sunulmaktadır.

Henoch-Schönlein purpura in an adult patient, presenting with severe nephrotic syndrome

Henoch-Schonlein Purpura (HSP) in adults is a rare clinical finding. Even though HSP nephritis frequently leads a course with asymptomatic urinary findings, presentation with severe nephrotic syndrome is quiet rare and associated with poor renal outcome. In this article, a patient who was admitted to the hospital with severe nephrotic syndrome and diagnosed with HSP nephritis is presented. He also achieved full remission with steroids and cyclophosphamide treatment.


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