İzole Persistan Sol Süperior Vena Kava

Persistan sol süperior vena kava normal popülasyonun %0,3-0,5’inde görülen venöz sistemin anatomik bir varyasyonudur. Sağda vena kava olmaması durumunda izole sol süperior vena kava olarak adlandırılır ve bu durum daha nadir olarak görülür(%0,09-0,013). Persistan sol süperior vena kava tek başına görülebilir ancak atrial septal defekt, tek atrium, ventriküler septal defekt, Fallot tetralojisi, aort koarktasyonu ve pulmoner stenoz gibi kardiyovasküler anormalliklerle de ilişkilidir. Büyük çoğunluğu semptom vermez ve insidental olarak bilgisayarlı tomografide veya santral venöz kateter yerleştirilirken tespit edilir. Bu durumun farkında olma santral venöz erişim, kardiyotorasik cerrahi ve kalp pili yerleştirmelerden kaynaklanabilecek olası komplikasyonlardan kaçınmayı sağlar.

Isolated persistent left superior vena cava

A persistent left-sided superior vena cava is an anatomic variation of the venous system which is seen in 0.3-0.5% of the normal population. In the absence of vena cava on the right, it is called isolated left superior vena cava and seen very rare (0.09-0.013%). It is observed in isolation but can be associated with other cardiovascular abnormalities including atrial septal defect, single atrium, ventricular septal defect, tetralogy of Fallot, coarctation of the aorta, pulmonary stenosis. The vast majority of cases are asymptomatic and diagnosed incidentally during CT scanning of the chest, or as a result of line placement. Awareness about this condition is important to avoid complications stems from central venous access, cardiothoracic surgeries, and pacemaker implantation.

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  • Referans1. Kemal HS, Gunsel A, Cerit L, Kocaoglu M, Duygu H. Isolated Persistent Left Superior Vena Cava, Sick Sinus Syndrome, and Challenging Pacemaker Implantation. Case reports in cardiology 2017;2017:9842524.Referans2. Motta-Leal-Filho JM, Motta CA, Pilan BF, Affonso BB. Persistent left superior vena cava. Ann Thorac Surg 2014;97(4):1453.Referans3. Beyhan M, Celikyay F, Yuksekkaya R, Almus F, Ozturk B, Inonu H. Multidetector computed tomography findings of persistent left superior vena cava: a report of five cases. Respir Case Rep 2014;3(1):60-65 Referans4. Pretorius PM, Gleeson FV. Case 74: right-sided superior vena cava draining into left atrium in a patient with persistent left-sided superior vena cava. Radiology 2004;232(3):730-734 Referans5. Smyth YM, Barrett CD, Fahy GJ. Biventricular pacemaker implant in a patient with persistent left sided superior vena cava. Heart 2005;91(11):1427. Referans6. Morgan LG, Gardner J and Calkins J. The incidental finding of a persistent left superior vena cava: implications for primary care providers case and review. Case Rep Med 2015; 2015:198754. Referans7. Ebink C, Bos LJ, Vonken EP, Velthuis BK, Cramer MJM. An unusual presentation with persistent left superior vena cava. Neth Heart J 2004;12(2):69-71.