Van der Knaap hastalığı: manyetik rezonans görüntüleme bulguları: olgu sunumu

Van der Knaap hastalığı, megalensefalik lökoensefalopati ve subkortikal kistlerle karakterize nadir bir antitedir. Bu yazıda Van der Knaap hastalığı'nın radyolojik ve klinik tanı kriterlerine sahip üç pediatrik olgunun beyin manyetik rezonans görüntüleme (MRG) ve manyetik rezonans spektroskopi (MRS) bulguları sunulmuştur.

Van der Knaap disease, characterized by megalencephalic leukoencephalopathy and subcortical cysts, is a rare condition. We present, in this study, cerebral magnetic resonance imaging (MRI) and MR spectroscopy (MRS) findings of three pediatric patients with radiological and clinical diagnostic criteria of this disease.

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