Zeliha FAZLIOĞULLARI, Nadire ÜNVER DOĞAN, Betül SEVİNDİK, Nusret SEHER, Ahmet KAĞAN KARABULUT

Tip B kesintili arkus aorta: olgu sunumu

Kesintili arkus aorta nadir rastlanan, fatal seyirli konjenital kardiyak bir anomali olup, aorta ascendens ile aorta descendens arasındaki bir segmentte atrezinin olması şeklinde tanımlanır ve %98 oranında diğer kardiovasküler anomalilerle birlikte bulunur. Üç tipi mevcuttur. Tip A’da kesinti, a. subclavia sinistra’nın distalindedir. Tip B’de, a. carotis communis sinistra ile a. subclavia sinistra, tip C’de, a. carotis communis sinistra ile a. carotis communis dextra arasındadır. Selçuk Üniversitesi pediatrik kardiyoloji kliniğine başvuran postnatal 5. gününde bir erkek bebeğin çekilen ekokardiyografisinde; truncus brachiocephalicus’un distalinden itibaren tip B kesintili arkus aorta, ventriküler septal defekt, biküspit aorta, patent ductus arteriosus, atrial septal defekt, annulus aorticus hipoplazisi tespit edildi. Bilgisayarlı tomografi anjiyografisinde ise, a. carotis communis sinistra ile a. subclavia sinistra arasında bağlantı olmadığı görüldü. Bu vakada, arcus aorta anomalisi ve eşlik eden diğer kardiovasküler anomalilerin erken tanı ve tedavisinde radyolojik görüntüleme yöntemlerinin önemi vurgulanmaktadır.

Interrupted aortic arch is a rare, fatal, congenital cardiac anomaly characterized by the presence of a segmental atresia between the descending and ascending aorta. In type A, the interruption is distal to left subclavian artery. In type B, between left common carotid artery and left subclavian artery; in type C, between left and right common carotid artery. Interrupted aortic arch is present to 98% with other cardiovascular anomalies. Echocardiography of a male baby at the 5th postnatal day referring to Selçuk University pediatric cardiology clinic revealed; type B interrupted aortic arch starting from distal truncus brachiocephalicus, ventricular septal defect, bicuspid aorta, patent ductus arteriosus, atrial septal defect and aortic annulus hipoplasia. The computer tomograpy angiography revealed interruption between left common carotid artery and left subclavian artery. This study highlights the importance of radiologic imaging methods in the early diagnosis and treatment of aortic arch anomaly and accompanying other cardiovascular anomalies.

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