Asemptomatik nadir kosta anomalileri: Kosta hipoplazileri olguları

Kostaların bilinen konjenital anomalileri ve deformiteleri arasında kosta füzyonları, iki kot arasında köprü oluşumu olması, bifid kostalar ve hipoplazik/aplazik kostalar sayılabilir. Bu morfolojik anomaliler ile anatomik varyasyonlar toplumda %0.15-0.31 arasında görülürler. Bu tür asemptomatik anomalilere örnek olması amacıyla yazıda kosta hipoplazisi mevcut olan üç vaka sunulmuştur. Farklı şikayetlerle hastaneye başvuran üç askerin akciğer grafilerinde kostal hipoplaziler görülmüştür. Hastaların hiçbirinde bir konjenital sendrom saptanmamıştır ve hipoplazilerin yarattığı bir şikayet mevcut değildir. Bilindiği üzere bu tür asemptomatik nadir kosta anomalilerinin genelde klinik önemi bulunmamaktadır, fakat tümöral veya inflamatuar kosta hastalıkları ile karıştırılmamaları için akciğer veya göğüs duvarıyla ilgilenen hekimler tarafından bilinmeleri ve akciğer grafilerinin bu tür anomalileri gözden kaçırmamak için daha dikkatli incelenmeleri gerekmektedir.

Asymptomatic rare rib anomalies: Cases of rib hypoplasia

There are various types of congenital anomalies and deformities of the ribs, including the developmental fusion of two or more ribs, the articulation or bridge formation between two ribs, bifid rib (forked rib) and hypoplastic/aplasic rib. These morphologic anomalies and anatomic variants occur in 0.15%–0.31% of the population. Here in this paper, three patients with rib hypoplasia were reported as examples of these rare asymptomatic anomalies. The chest X-rays of three soldiers presenting with several other complaints revealed rib hypoplasias. None of the patients had a congenital disease, and they had no complaints related to these rib hypoplasias. As it is known, these rare rib anomalies are usually of little or no clinical significance; however, any physician dealing with the lung and the chest wall should be familiar with these rare anomalies to distinguish them from any tumoral or inflammatory rib diseases, and the chest X-rays should be examined very carefully to detect such asymptomatic rib anomalies.

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Fırat Tıp Dergisi-Cover
  • ISSN: 1300-9818
  • Başlangıç: 2015
  • Yayıncı: Fırat Üniversitesi Tıp Fakültesi