Hemochromatosis, although increasingly recognized by clinicians, is still underdiagnosed because it is often considered a rare disorder. The fully established disease consists of cirrhosis, diabetes, and skin pigmentation (bronze diabetes). Diabetes can occur as a result of direct islet cell damage due to iron infiltration. Presentation with diabetic ketoacidosis is rare, and only few cases have been reported. This case report is of a patient with hemochromatosis presenting with diabetic ketoacidosis.
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