Renal tubuler asidoza bağlı hipokalemik periodik paralizi
Distal renal tubüler asidoz; hipokalemi, hiperkloremik metabolik asidoz ve idrar pH'sının 5.8'in üzerinde olması ile karakterize metabolik bir hastalıktır. Bu bulgulara hiperkalsüri, nefrokalsinozis, nefrolitiazis, sağırlık, osteomalazi veya rikets bulguları eşlik edebilir. Renal tübüler asidozda laboratuvar bulgusu olarak hipokalemi sık görülmesine karşın, bu eksikliğin klinik bulgusu olan güçsüzlük nadir görülmektedir. Bu makalede polikliniğimize güçsüzlük yakınması ile başvuran ve etyolojik taramalar sonucu distal renal tübüler asidoza sekonder hipokalemi tesbit edilen sporadik bir olgu sunulmuştur.
Hypokalemic periodic paralysis due to renal tubuler asidosis
Distal tubular acidosis is a metabolic disorder which is characterized by hypokalemia, hyperchloremic metabolic acidosis, urine pH above 5.8. These findings may be accompanied by hypercalciuria, nephrocalcinosis, nephrolithiasis, deafness, osteomalacia, or rickets. Whereas hypokalemia is frequently seen in renal tubular acidosis weakness due to hypokalemia is rarely seen. In this article, a sporadic case who was admitted to our clinic with the complaint of weakness and diagnosed as hypokalemia secondary to distal renal tubular acidosis was presented.
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