Murat ULUKUŞ, Mustafa ULUKUŞ, Tavmergen Ege Nazan GÖKER, Mustafa Coşan TEREK, Osman ZEKİOĞLU

Mayer-rokitansky-kuster-hauser syndrome with a borderline ovarian serous cystadenoma: A case report

Mayer-Rokitansky-Kuster-Hauser (MRKH) sendromu, vagina ile uterusun beraberce hipoplazisi olarak bilinmektedir ve 4000-5000 dişi doğumda 1 olarak gözlenmektedir. Primer amenore, sterilite ve pelvik ağrı gibi belli başlı jinekolojik problemlere yol açan bu sendromun tanısı, cerrahi eksplorasyonla olduğu kadar, günümüzde gelişen görüntüleme teknikleri ile de mümkün olabilmektedir. Bu makalede kliniğimize üç gündür süren alt kadran ağrısı şikayeti ile başvuran ve yapılan tetkikler sonucunda MRKH ile birlikte överde borderline seröz kistadenom saptanan 43 yaşında bir olgu sunulmuştur.

Anahtar Kelimeler:

Kadın doğum cerrahi işlemleri, Yumurtalık neoplazmları, Orta Yaş

Mayer-rokitansky-kuster-hauser sendromlu bir olguda izlenen overin borderline seröz kistadenomu: Olgu sunumu

The Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome comprises the combined hypoplasia of the vagina and the uterus and it occurs in 1 of 4000-5000 female births. It may cause many gynecological problems such as primary amenorrhea, sterility, pelvic pain and can be diagnosed by screening or surgical methods. We report a 43-year-old women with MRKH syndrome and an ovarian serous borderline cystadenoma. She was admitted to our clinic complaining of lower abdominal pain for three days.

Keywords:

Obstetric Surgical Procedures, Ovarian Neoplasms, Middle Age,

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1. Giatras K, Licciarddi F, Grifo JA: Laparoscopy for pelvic pain in the Mayer-Rokitansky-Kuster-Hauser syndrome. J Reprod Med 1998:43:203-205.
2. Koonings PP, Al-Marayati L, Schlaert JB, Lobo RA: Mayer-Rokitansky-Kuster-Haüser syndrome associated with endodermal sinus tumor of the ovary. Fertil Steril 1991 ;56:577-578.
3. Fisher K, Esham RH, Thorneycroft I: Scoliosis associated with typical Mayer-Rokitansky-Kuster-Hauser syndrome. South Med J 2000:93:243-246.
4. Tsaur GT, Lee MH, Su SL, Wu, MJ, Huang TW: Mayer-Rokitansky-Kuster-Hauser syndrome with immature teratoma of the ovary at age 4 years. Gynecol Oncol 1995;56: 456-459.
5. Strubbe EH, Willemsen WN, Lemmens JA, Thijn CJ, Rolland R: Mayer-Rokitansky-Kuster-Hauser syndrome: distinction between two forms based on excretory urographic, sonographic and laparoscopic findings. Am J Roentgenol 1993; 160: 331-334.
6. Strubbe EH, Cremers CW, Willemsen WN, Rolland R, Thijn CJ: The Mayer-Rokitansky-Kuster-Hauser syndrome without and with associated features: two separate entities? Clin Dysmorphol 1994;3:192-199.
7. Russ PD, Allen-Davis JT, Weingardt JP, Anderson MS, Koyle MA: Mayer-Rokitansky-Kuster-Hauser syndrome diagnosed by magnetic resonance imaging in a 15-year-old girl. J Pediatr Adolesc Gynecol 1997; 10: 89-92.
8. Fedele L, Dorta M, Brioschi D, Giudici MN, Candiani GB: Magnetic resonance imaging in Mayer-Rokitansky-Kuster-Hauser syndrome. Obstet Gynecol 1990; 76: 593-596.