Münevver OKAY, Buse Rahime HISARCI, İlknur Aydın CANTÜRK, Dilek AĞIRCAN, Abdülkadir KOÇER

IVIG tedavisine dramatik yanıt veren dermatomiyozit olgusu

Dermatomiyozit (DM), bir idiyopatik inflamatuar miyopati ve nadir görülen bağ doku hastalıklarından olup cilt lezyonları ile karakterizedir. DM tanısı için karakteristik raşlara ilaveten proksimal kas güçsüzlüğü ve kas enzim düzeylerinin artışı gibi kriterlere gerek duyulmaktadır. Bu yazıda 26 yaşında kas güçsüzlüğü ve tipik cilt lezyonları ile başvuran ve IVIG tedavisine dramatik yanıt veren dermatomiyozit olgusu sunulmuştur

A case of dermatomyositis with a dramatic response to IVIG treatment

Dermatomiyozitis (DM) is an idiopathic inflammatory myopathy and a rare connective tissue disease which is characterized by skin lesions. Diagnosis of DM requires a characteristic rash and other criteria, such as proximal muscle weakness and muscle enzyme level elevation. In this paper we present a twenty-six-year-old man who attended with muscle weakness, typical skin manifestations and providing a dramatic response to IVIG treatment of dermatomyositiz

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