Huge fetal sacrococcygeal teratoma: Antenatal and postnatal management

Sacrococcygeal teratoma (SCT) is one of the most common fetal tumors (1/30000). Ultrasonography is an important method for diagnosis and following the SCT. Pregnancy can be managed by diagnosing the teratoma, monitoring its growth rate and fetal complications with the USG. Some complications such as fetal hydrops, dystocia, hemorrhage and rupture can be seen. In this report, we present a 25 year old woman with 25 weeks gestation according to her last menstrual date. We determined a 5x4 cm of sacrococcygeal teratoma through ultrasonographic examination. Because of the acute enlargement of the sacrococcygeal teratoma, a cesarian section was performed without complication at 36 gestational weeks with no fetal compromise developing such as fetal hydrops or placentomegaly. The fetus underwent surgery in the pediatric surgery. The sacrococcygeal teratoma was removed and the histopathology revealed immature teratoma. Neonates with SCT after exicision require long-term follow up for functional impairment. Management of the sacrococcygeal tumors are required with a multidiciplinal approach by the obstetrician, pediatrist and pediatric surgeon.

Dev fetal sakrokoksigeal teratom: Antenatal ve postnatal yönetim

Sakrokoksigeal teratom, fetal tümörler arasında yaygın izlenen (1/30000) tümörlerden biridir. Tanı ve takipte ultrasonografi en önemli yöntemdir. Fetal sakrokosigeal teratom tanısı konan gebelikler takip edilebilir. Bu gebeliklerde tümörün büyüme hızı ve fetal komplikasyonlar ultrasonografi ile izlenir. Fetal hidrops, distosi, kanama ve rüptür gibi komplikasyonlar görülebilir. Makalemizde 25 yaşında, 25. gebelik haftasında ultrasonografi ile değerlendirmede 5x4 cm büyüklüğünde fetal sakrokoksigeal teratom saptanan hastamızı sunduk. Tümörün ani hızlı büyümesi nedeniyle, fetal hidrops veya plasentomegali gibi komplikasyonlar gelişmemişken gebeliğin 36 haftasında sezeryan ile komplikasyonsuz olarak doğum gerçekleştirildi. Yenidoğan, pediatrik cerrahi kliniğinde öpere edildi. Tümör çıkartıldı ve histopatolojik değerlendirmesi immatür teratom olarak saptandı. Öpere edilen yenidoğan/ar uzun dönem fonksiyonel bozulmalar açısından takip edilmelidir. Sakrokoksigeal teratomlu hastaların yönetimi obstetrisyen, pediatrist ve pediatrik cerrahı içeren multidisipliner yaklaşımı gerektirmektedir.

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Ege Tıp Dergisi-Cover
  • ISSN: 1016-9113
  • Yayın Aralığı: Yılda 4 Sayı
  • Başlangıç: 1962
  • Yayıncı: Ersin HACIOĞLU