Korkut N. BIÇAK, F.E. BAYAM, Z. ÇOLAKOĞLU

Ganglionopati nedeni: Sjogren sendromlu olgu

Bilimsel Zemin: Sjögren sendromu, sekretuar bezlerde mononükleer hücre infiltrasyonu ile giden kronik inflamatuar, otoimmun bir egzokrinopatidir. Hastaların %10-40 da merkezi sinir sistemi ya da periferik sinir sistemi etkilenimi şeklinde nörolojik tutulum görülebilir. Gereç ve Yöntem: Hastanın rutin nörolojik muayenesi, biokimyasal incelemeler, serolojik testler, vaskülit belirteçleri, troid fonksiyon testleri, B12 ve E vitamini seviyeleri , BOS incelemesi ve Schirmer testi yapıldı. Sonuç: Sjögren sendromunun nörolojik komplikasyonları arasında ganglionopati iyi bilinen ancak çok nadir görülen bir tablodur. Sunulan olgu klasik Sjögren kliniği ortaya çıkmadan ganglionopati gibi nörolojik komplikasyonların ortaya çıkabileceğini göstermiştir.

Anahtar Kelimeler:

Yürüyüş şekli, Sjogren sendromu, Elektrofizyolojik olay, Erişkin, Kadın

Sjogren syndrome presenting with ganglionopathy

Scientific background: Sjogren Syndrome is a chronic autoimmune disorder of the exocrine glands with associated lymphocytic infiltrates of the affected glands. Neurological involvement occurs in approximately 10-40 % of patients with Sjogren syndrome. Materials and methods: Routine neurologic examination, biochemical screen, serological tests, vasculitic markers, thyroid function tests, B12 and vitamine E levels, CSF screen and Schirmer tests was conducted in the patient. Conclusions: The ganglionopathie is a rare but well known problems of the Sjogren Syndrome. The case which is presented has shown that before the clinics of classic sjogren disease comes out, some neurological complications such as ganglionopathy might appear.

Keywords:

Gait, Sjogren's Syndrome, Electrophysiological Phenomena, Adult, Female,

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