Cushing hastalığı ile birlikte dev adrenal myelolipoma - Olgu sunumu

Adrenal myelolipoma nadir, benign ve endokrin olarak inaktif tümörlerdir. Genellikle rutin görüntülemelerde ya da otopsi sırasında insidental olarak bulunurlar. Adrenal myelolipomaların çoğu küçük (çapı

Anahtar Kelimeler:

Böbrek üstü bezi neoplazmları, Miyelolipom, Hipofiz ACTH hipersekresyonu

Giant adrenal myelolipoma associated with Cushing's disease: Case report

Adrenal myelolipoma is a rare, benign, endocrinologically inactive and asymptomatic tumor which is usually found incidentally at imaging or autopsy. Most adrenal myelolipomas are small (diameter <5 cm) unilateral and asymptomatic. Symptomatic tumors are very rare. They may be associated with an endocrine disorder such as Cushing's disease. US, CT, MRI, are the most effective diagnostic methods. Usually adrenal myelolipoma needs no treatment. But in cases with symptomatic, large sized and any suspicioun related with the diagnosis, the mass should be surgically removed. We reported a case of giant adrenal myelolipoma associated with Cushing's disease in a 51- year- old woman. Imaging studies identified a mass measuring 14x10 cm on the left adrenal which was surgically removed.

Keywords:

Adrenal Gland Neoplasms, Myelolipoma, Pituitary ACTH Hypersecretion,

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