Ailevi Akdeniz ateşi ve periarteritis nodosa birlikteliğinde gelişen karaciğer ve böbrekte subkapsüler hematom ve hemanjiom rüptürü

Ailevi Akdeniz Atesi (FMF) ve periarteritis nodosa (PAN) hastalığı beraber seyrettiğinde, renal ve hepatik spontan subkapsüler hematom gelisme riski artar. Bu durum hayatı tehdit edebilen ciddi bir tablodur. FMF tanısı alan hastalarda PAN ile ilgili semptom ve bulguların tabloya eklenmesi durumunda subkapsüler hematom gelisme ihtimali nedeniyle dikkatli olunmalıdır. Ultrasonografi ve bilgisayarlı tomografi, erken asamada subkapsüler hematomu ve miktarını tespit etmede önemlidir. Burada, FMF tanısı almıs ve önceden bilinen karaciğer hemanjiomu bulunan 17 yasında erkek hastada, es zamanlı olarak gelisen perirenal/subkapsüler hematom ile karaciğerde rüptüre hemanjiom ve subkapsüler hematomun radyolojik bulguları sunulmaktadır.

Hepatic and renal subcapsullary haematoma and hemangioma rupture in a familial Mediterranean fever and periarteritis nodosa patient

When familial Mediterranean fever (FMF) and periarteritis nodosa (PAN) coexist, risk of spontaneous subcapsular haematoma increases. This is a life threatening condition. In patients with a diagnosis of FMF, when signs and symptoms of PAN is added, one should be careful about subcapsular haematoma. Ultrasonography and computerized tomography, are important, in detecting and measuring amount of subcapsular haematoma in early stages Herein, we report a 17 year old patient with a previous diagnosis of FMF and hepatic hemangioma to have concomitant subcapsular/perirenal haematoma and ruptured hepatic hemangioma. Radiological findings in ruptured hepatic hemangioma are discussed.

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