Anesthesia management in a patient with Carney Syndrome: Case report

ISSN: 1301-0883
Başlangıç: 1996
Yayıncı: ERBİL KARAMAN

Carney Syndrome is a complex of symptoms which can demonstrate autosomal dominant or sporadic transition that are followed by cardiac and cutaneous myxomas and endocrine abnormal activity. Myxomas demonstrate familial transition due to autosomal dominant inheritance at a rate approximately of 5%. In anesthesia management, some of the significant things to be paid attention to are; the localization, size and mobility of the myxoma. Rate of familial myxoma after surgical resection is about 21-67%. In this article, anesthesia practice in a Carney Syndrome case with cerebral aneurysms that is scheduled for operation due to surrenalectomy, has been presented.

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