Recep ÖZTÜRK, Mehmet Akif ŞİMŞEK, Ömer Faruk ATEŞ, Ayşe Tuğçenur GENÇOĞLU, Coşkun ULUCAKÖY

NÖROFİBROMATOZİS İLİŞKİSİZ MULTIPLE SCHWANNOMA

Bu yazı, nörofibromatozis (NF) özellikleri olmayan bir multiple schwannoma olgusu raporudur. Hastane bilgi sistemi kayıtları ve hasta dosyasından hastanın öyküsü, fizik muayene bulguları, radyolojik ve histopatolojik inceleme bulguları incelendi. Hastanın ve ailesinin NF öyküsü yoktu. Semptomatik lezyonların tümüne total eksizyon yapıldı. Histopatolojik inceleme, tüm lezyonları schwannom olarak doğruladı. Hastanın post-operatif on ikinci ayında yeni lezyonu yok ve yaşamından memnundur. Nörofibromatozis tip 2 ile ilişkisiz olup, multipl lezyonlar şeklinde ortaya çıkan schwannomlar nadirdir. Yazarlar semptomatik lezyonlarda cerrahi eksizyon önermektedir.

Anahtar Kelimeler:

nörofibromatozis, schwannomatozis, multiple primer schwannomalar

Multiple schwannoma unrelated with neurofibromatosis

This is a report of a case of multiple schwannoma without any neurofibromatosis (NF) patterns. Patient’s history, physical examination findings, radiological and histopathological examination findings were evaluated using the records of the hospital information system and the patient’s file. The patient and his family did not have a history of NF. Excision of all symptomatic lesions was performed. Histopathological examination confirmed all lesions as schwannoma. The patient does not have a new lesion on his twenty forth postoperative month and he is satisfied with his life. The disease that is present with multiple schwannomas and that is not related with neurofibromatosis type 2 is rare. The authors recommend surgical excision for symptomatic lesions.

Keywords:

neurofibromatosis, schwannomatosis, multiple primary schwannomas,

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