Derya Fatma BULUT, Gülen Gül MERT, Faruk İNCECİK, Özlem Mihriban HERGÜNER, Şakir ALTUNBAŞAK

Tekrarlayan Fasiyal Paralizili bir olgu: Melkersson-Rosenthal Sendromu

Melkersson-Rosenthal sendromu (MRS), tekrarlayan fasiyal paralizi, orofasiyal ödem, dilde fissürle karakterize nadir bir nöromukokütanöz sendromdur. Oligosemptomatik ve monosemptomatik olgular, klasik triaddan sık görülür. Bulguların ikisinin görülmesi veya bulguların biri ve biyopside granülomatöz keilitin varlığı Melkersson-Rosenthal sendromu tanısı için yeterlidir. Bu yazıda Melkersson-Rosenthal sendromu tanısı alan 12 yaşında bir erkek sunulmuştur.

Anahtar Kelimeler:

Melkersson-Rosenthal sendromu, tekrarlayan fasiyal paralizi, çocuklar.

A Case with Recurrent Facial Palsy: Melkersson-Rosenthal Syndrome

Melkersson-Rosenthal syndrome (MRS) is a rare neuromucocutaneous syndrome characterized by recurrent facial paralysis, orofacial edema and fissured tongue. Oligosymptomatic and monosymptomatic forms are more common than the triad. The presence of two manifestations or one manifestation with granulomatous cheilitis in biopsy is sufficient to make diagnosis of Melkersson-Rosenthal syndrome. We present a 12 years-old male who is diagnosed Melkersson-Rosenthal syndrome.

Keywords:

Melkersson-Rosenthal syndrome, recurrent facial paralysis, children.,

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