Kemal NİŞLİ, Aygün DİNDAR, Şeref OLGAR, Naci ÖNER, Eker Rukiye ÖMEROĞLU, Türkan ERTUĞRUL, Atıf AKÇEVİN

Hemitrunkus: Ender bir doğumsal kalp hastalığı

Pulmoner arter dallarından birinin çıkan aortadan kaynaklanması hemitrunkus arteriozus (HA) olarak adlandırılır. Bu doğumsal kalp hastalığı çok ender olarak görülür. Bu yazıda sağ pulmoner arteri çıkan aortadan kaynak alan ve bir aylıkken ekokardiyografi ile tanı konan bir HA vakası sunulmuştur. Vakada, hemiturunkus ile beraber patent duktus arteriozus, patent foramen ovale ve sağ arkus aorta da tespit edilmiş. HA tanısı kardiyak kateterizasyon ile doğrulanmıştır. Bu ender doğumsal kalp hastalığında erken tanı ve cerrahi düzeltme zorunluluğu vurgulanmıştır.

Anahtar Kelimeler:

Hipertansiyon, Kalp kusuru, doğuştan, Süt çocuğu, yenidoğan, Pulmoner arter

Hemitruncus: A rare congenital heart defect

Ascending aortic origin of a branch of pulmonary artery is also named as hemitruncus arteriosus (HA). It is a very rare congenital heart defect. We report a case with HA whose right pulmonary artery was arising from the ascending aorta. The diagnosis was made by echocardiography at the age of one month. In addition the patient had patent ductus arteriosus, patent foramen ovale and right aortic arcus. The diagnosis of HA was confirmed by cardiac catheterization. Early diagnosis surgical correction of this rare congenital heart defect is mandatory.

Keywords:

Hypertension, Heart Defects, Congenital, Infant, Newborn, Pulmonary Artery,

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