Kistik Fibrozise Bağlı Gelişen Diyabette Tıbbi Beslenme Tedavisi: Bir Olgu Sunumu

Kistik fibrozis otozomal resesif geçişli, kronik ve ilerleyici, temel olarak akciğer ve pankreas olmak üzere birden çok organ hasarıyla karakterize kalıtsal bir hastalıktır. Kistik fibrozis hastalığında yaş ilerledikçe önce ekzokrin işlevlerinde sonra endokrin işlevlerinde bozulmanın sonucunda adacık hücreleri zarar görmekte ve insülin eksikliği ortaya çıkmaktadır. Kistik fibrozisli hastalarda kistik fibrozise bağlı diyabet (KFBD), orta yaş döneminde yaygın görülen komplikasyonlardandır. KFBD tedavisinde temel hedef, diyabet diyeti ve kistik fibrozis diyetini birleştirerek enerjisi, proteini ve yağı yüksek insülin kullanmayan hastalarda glisemik indeksi düşük diyet planı ile normoglisemiyi ve yeterli gelişimi sağlamaktır. Bu olgu sunumunda kistik fibrozise eşlik eden hiperglisemi, malnütrisyon ve osteopeni tanısı ile izlenen olgunun hastanedeki tedavisinde tıbbi beslenme tedavisi ile insülin rejimine gerek duyulmadan kan glukoz kontrolünün sağlanabildiği gösterilmiş ve tıbbi beslenme tedavisinin yönetimi tartışılmıştır

Medical Nutrition Therapy in Diabetes Mellitus Related to Cystic Fibrosis: A Case Report

Cystic fibrosis is an autosomal recessive, chronic, progressive inherited disease, characterized primarily by multiple organ injury, mainly lung and pancreas. As age progresses in cystic fibrosis disease, the islet cells are damaged and insulin deficiency arises, as a result of degradation of first in exocrine functions and then in endocrine functions. Cystic fibrosis-associated diabetes in patients with cystic fibrosis is a common complication in the middle ages. The main aim in the treatment of cystic fibrosis-associated diabetes is to combine diabetes diet and cystic fibrosis diet. In this way, with the diet plan which has low glycemic index in patients who do not use insulin provide normoglysemia and adequate development. In this case report, it was shown that glucose control of cystic fibrosis patient, accompanied by hyperglycaemia, malnutrition and osteopenia diagnosis, can be achieved with medical nutrition therapy, without the use of insulin. Additionally management of medical nutrition treatment was discussed

Kaynakça

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