N. Ferah DÖNMEZ, Oya KILCI, Canan ÜN, Derya TÜRKASLAN, Tolga BARUT, Bayazıt DİKMEN

Konjenital afibrinojenemili olguda akut batın nedeniyle anestezi deneyimimiz

Konjenital afibrinojenemi nadir görülen herediter bir koagülasyon bozukluğudur. Klinikte asemptomatik olabileceği gibi, minimal kanamaya eğilimden hayatı tehdit edecek kanamalara ya da tromboembolik olaylara sebep olarak da kendini gösterebilir. Bu olguda, konjenital afibrinojenemi hastasında akut batın nedeniyle yapılan acil operasyondaki anestezi deneyimimizi anlatmak istedik.

Our experience of anesthesia in a patient with congenital afibrinogenemia undergoing acute abdominal surgery

Congenital afibrinogenemia is a rare inherited coagulation disorder. As it can be asymptomatic, its clinical manifestations vary from minimal tendency of bleeding to life-threatening bleedings or thromboembolic events. In this case, we want to share our anesthesia experience in a patient with congenital afibrinogenemia who has undergone acute abdominal surgery.

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