Hacer SERDAROĞLU, Saban YALÇIN, Süer Gülseren KAYA, Asuman UYSALEL

Dwarfizmli gebede anestezi tecrübemiz

Pek çok farklı tipi olan dwarfizmin en yaygın formu akondroplazik dwarfizmdir. Bu hastalar 148 cm'den daha kısa boya sahiptirler, %80'i gen mutasyonuna bağlı sporadik olgulardır. Endokondral kemik formasyonunun bozulması nedeniyle spinal ve kraniofasiyal anormalliklerle seyreder. Kadınlar erkeklerden daha çok etkilenir ve normal bireylere göre fertiliteleri daha düşüktür. Dwarfizmli olguların operasyon öncesi hazırlıklarında anatomik anormallikler nedeniyle zor havayolu olabileceği göz önünde bulunurularak gerekli hazırlıklar yapılmalıdır. Bu olgu sunumunda 29 yaşında dwarfizmli hastanın elektif sezaryanındaki anestezi tecrübemizi aktarmayı amaçlandık.

Anesthetic management of a pregnant with dwarfism

Dwarfism has many different types, the most common form is achondroplasic dwarfism. These patients are shorter than 148 cm. 80% of cases are sporadic cases due to gene mutations. Spinal and craniofacial abnormalities have seen due to impaired endochondral bone formation. Women are more affected than men and the fertility rate is lower than normal subjects. In pre-operative preparation of dwarfism cases, necessary preparations should be taken into account for diffucult airway due to various anatomical abnormalities. In this case report, we aimed to present our anesthetic experience in caeserian section of a 29 years old dwarfic patient.

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