Hasan SAYGIN, Yağmur ÇANKAYA, FİLİZ ALKAYA SOLMAZ, PAKİZE KIRDEMİR

DÜŞÜK DOZ TİYOPENTAL İLE HUNTINGTON KORESİNDE ANESTEZİ YÖNETİMİ: BİR OLGU SUNUMU

Huntington koresi sinir sisteminin nadir görülen genetik geçiflli bir hastalığıdır. Otozomal dominant geçiflli olan bu hastalık ilerleyici kore, demans ve psikiyatrik bozukluklarla karakterizedir. Huntington koresi hastalarının faringeal disfonksiyon ve artmıfl aspirasyon riski ideal anestezi tekniğini seçmeyi zorlafltırmaktadır. Bu hastalar için genel anestezinin ilk hedefi hava yolunun korunması ve hızlı ve güvenli derlenmeyi sağlamaktır. Olgumuz 59 yaflında bayan hasta genel anestezi altında subdural hematomu boflaltıldı. ndüksiyonda midazolam, remi fentanil, tiyopental ve rokuronyum kullanıldı. Anestezi idamesi desfluranla sağlandı. Düflük doz tiyopental (4 mg kg-1) kullanıldı, antikolinerjik ajanlardan kaçınıldı. Operasyon sonunda spontan solunumu geldikten sonra 60. dakikada ekstube edildi ve servise gönderilidi.

LOW DOSE THIOPENTAL ANESTHETIC MANAGEMENT OF A PATIENT WITH HUNTINGTONS CHOREA: A CASE REPORT

Huntington's chorea is a rare hereditary disorder of the nervous system. It is inherited as an autosomal dominant disorder and is characterized by progressive chorea, dementia and psychiatric disturbances. Huntington's chorea in patients with pharyngeal dysfunction and increased risk of aspiration makes it di fficult to decide on the ideal anesthetic technique. The primary goal in general anesthesia for these patients is to provide airway protection and a rapid and safe recovery. In our case, a 59 year old female patient under general anesthesia with cases of subdural hematoma was evacuated, midazolam, remi fentanil, tiopental and rocuronium were used, maintenance of anesthesia with desflurane was provided. Low dose of thiopental (4 mg kg-1) was used, anticholinergic agents were avoided. At the end of operation after the occurance of spontaneus breathing, patient was extubated in 60 minutes and returned to service

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