Osman Z. ŞAHİN, Fatih TEKİN, Zeki KARASU, Yücel BATUR, Deniz NART

Hemofagositik sendrom ve fulminan hepatit

Hemofagositik sendrom; makrofajların kan hücrelerini fagosite etmesiyle karakterize ve ateş, hepatosplenomegali, pansitopeni gibi bulgularla kendini gösteren klinik bir tablodur. Hemofagositik sendromun etyolojisinde başlıca enfeksiyonlar, hematolojik maliniteler ve bağ doku hastalı kları yer almaktadır. Bu yazıda hemofagositik sendrom ve fulminan hepatit birlikteliği gösteren bir olgu sunulmaktadır.

Anahtar Kelimeler:

Hemofagositik sendrom, hemofagositoz, fulminan hepatit

Hemophagocytic syndrome and fulminant hepatic failure

Hemophagocytic syndrome is a clinical manifestation of hemophagocytosis that is characterized by high fever, hepatosplenomegaly, and pancytopenia. Infections, hematological malignancies and connective tissue diseases are the main etiological factors of hemophagocytic syndrome. In this article, we present a case with fulminant hepatic failure associated with hemophagocytic syndrome.

Keywords:

Hemophagocytic syndrome, hemophagocytosis, fulminant hepatic failure,

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