A rare clinical entity: Two cases of retroperitoneal fibrosis with different approach and consequences

Retroperitoneal fibroz, kronik inşamasyon ve belirgin fibroz içeren sıklıkla üreterleri ya da diğer intraabdominal organları çevreleyen retroperitoneal bir dokunun varlığı ile karakterize nadir bir hastalıktır. Erken dönem semptomları karında ve lumbar bölgede rahatsızlık şeklinde nonpesifik özelliktedir. Fibroz ilerledikçe oluşan bası etkisi septomlarda artışı belirler. Nadir bir klinik durum olması ve klinik ve fizik muayene bulgularının nonspesifik olması çoğu zaman teşhisi geciktirir ve kalıcı organ yetmezliği ve mortaliteye yol açar. Biz burada hastalığın farklı evrelerinde tanı almış ve farklı şekillerde sonuçlanmış iki retroperitoneal fibroz olgusunu sunduk. Amacımız erken teşhisin organ fonksiyonlarını korumadaki önemini vurgulamaktır.

Nadir bir klinik durum: Farkl› yaklafl›m ve sonlan›mlarla iki retroperitoneal fibrozis olgusu

Retroperitoneal fibrosis is a rare disease, characterized by the presen- ce of a retroperitoneal tissue, consisting of chronic inflammation and marked fibrosis, which often entraps the ureters or other abdominal organs. Early symptoms are nonspecific as abdominal or lumbar dis- comfort. As the fibrosis progresses, the compressive effects determi- ne the symptomatic evolution. Retroperitoneal fibrosis diagnosis is usually delayed, which can result in permanent organ failure and mor- tality. We present herein two cases of retroperitoneal fibrosis diagno- sed in different stages of the disease and resulting in different outco- mes. Our aim is to stress the importance of early diagnosis in preser- ving organ function.

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