A giant clear cell sarcoma on right scapular: A case report

Clear-cell sarcoma is a rare and malignant soft tissue tumor most commonly located at the distal end ofextremities and rarely at the trunk. Data on the clinical features of the tumor is limited, complicating theanalysis of prognosis and establishment of treatment protocols.In our study, we present a case diagnosed with clear-cell sarcoma in his right scapula and treated withtumor resection and chemotherapy, combination of dacarbazine, pharmorubicin and cisplatin. The patient died due to multiple organ failure eight months after operation. Early diagnosis, attentive care, andextended surgical resection combined with adjuvant therapy is of essence in treatment of clear-cellsarcoma.© 2016 Turkish Association of Orthopaedics and Traumatology. Publishing services by Elsevier B.V. This isan open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/)

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