KARDIYOVASKÜLER HASTALIĞA BAĞLI SES KISIKLIĞI: PULMONER ARTER ANEVRIZMASI VE DEV ATRIYUMLARI OLAN BIR HASTADA KARDIYOVOKAL SENDROM

Kardiyovokal sendrom veya Ortner sendromu genişlemiş kardiyak yapıların sıkıştırmasına sonucu gelişen sol laringeal rekürren sinir palsisine bağlı ses kısıklığıdır. Mitral kapak hastalığı ile olan genişlemiş sol atriyum bu nadir sendromun iyi bilinen sebebidir ancak başka kardiyovasküler durumlarda patogeneze katkida bulunabilmektedir. Mevcut veriler sadece genişlemiş sol atriyumun değil, sol rekürren laringeal sinirin genişlemiş hipertansif pulmoner arter, aorta ve ligamentum arteriosum arasında sıkıştığını göstermektedir. Bu bağlamda, pulmoner arter anevrizması ve dev atriyumları ve düzeltilmiş atriyal septal defekti olan bir hastada kardiyovokal sendrom olgusunu sunduk. Hasta iki yıldır kademeli olarak artan ses kısıklığı ile başvurdu ve laringoskopide sol vokal kord paralizi tespit edildi. Transtorasik ekokardiyografi ile yapılan kardiyovasküler incelemede, kardiyovokal sendrom ile uyumlu olarak pulmoner arter anevrizması ve dev atriyumlar mevcuttu

Hoarseness Secondary To Cardiovascular Disease: Cardiovocal Sydrome In a Patient With Pulmonary Artery Aneurysm and Giant Atria

Cardiovocal syndrome or Ortner syndrome is the hoarseness secondary to recurrent laryngeal nerve palsy due to compression enlarged cardiovascular structures. Dilated left atrium with mitral valve disease is a well-known cause for this rare syndrome; however several cardiovascular conditions also contribute to the pathogenesis. Data suggest that, recurrent laryngeal nerve seems to be compressed in the window between enlarged hypertensive pulmonary artery, aorta and ligamentum arteriosum not solely by enlarged left atrium. In this context, we presented a case of cardiovocal syndrome in a patient with pulmonary artery aneurysm, giant atria and corrected atrial septal defect. The patient was admitted for gradual hoarseness for two years and laryngoscopy revealed left vocal cord paralysis. Cardiovascular examination with transthoracic echocardiography showed pulmonary artery aneurysm with giant atria which is compatible with cardiovocal syndrome

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Acıbadem Üniversitesi Sağlık Bilimleri Dergisi-Cover
  • ISSN: 1309-470X
  • Yayın Aralığı: Yılda 4 Sayı
  • Başlangıç: 2010
  • Yayıncı: ACIBADEM MEHMET ALİ AYDINLAR ÜNİVERSİTESİ