Melikhan ÇERÇİ, Begül YAĞCI-KÜPELİ, Ali İhsan ÖKTEN, Kerem Mazhar ÖZSOY, Tamer ÇELİK, Fulya ADAMHASAN, Ümit ÇELİK, Suzan ZORLUDEMİR, Serhan KÜPELİ

Transvers miyelitle gelen bir primer spinal kord glioblastoma multiforme vakası

Primer spinal kord tümörlerine çocukluk çağında nadiren rastlanır. Ependimomlar ve pilositik astrositomlar bunların başında gelir. Spinal glioblastoma multiforme pediatrik intramedüller tümörlerin %1-3'ünü oluşturan nadir bir antitedir.Bu yazıda sırt ağrısı, paraparezi, yürüme bozukluğu ve sfinkter fonksiyon kaybı ile başvuran ve başlangıçta transvers miyelit olarak değerlendirilen 3 yaş 8 aylık erkek hasta sunulmuştur. Klinisyenlere bu şekilde transvers miyelit bulgularıyla başvuran vakalarda intramedüller tümörlerin de ayırıcı tanıda akılda tutulması gerektiği önerilmiştir.

Anahtar Kelimeler:

Spinal kord tümörleri, glioblastoma multiforme, transverse myelitis, çocukluk çağı

Primary spinal cord glioblastoma multiforme presenting with transverse myelitis

Primary spinal cord tumors are rarely encountered in childhood period. Ependymomas and pilocytic astrocytomas comprise the majority of spinal cord tumors in children. Spinal glioblastoma multiforme (GM) (grade IV astrocytoma) is a rare clinical entity accounting for only 1-3% of all pediatric intramedullary tumors. We report a 3- year-8- month-old male with primary spinal cord GM who presented with back pain, paraparesis, gait disturbance and loss of sphincter control and initially diagnosed as transverse myelitis.

Keywords:

Spinal cord tumors, glioblastoma multiforme, transverse myelitis, childhood,

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Yazışma Adresi / Address for Correspondence: Dr. Serhan Küpeli, Çukurova University, Faculty of Medicine, Department of Pediatric Oncology, ADANA GSM: 905327616752
Email: serkupeli@yahoo.com G eliş tarihi/Received on: 31.09.2013
Kabul tarihi/Accepted on:07.11.2013