Olcay ÜNVER, Zehra İşık HASILOĞLU, Sezgin ŞAHİN, Mehmet Sait ALBAYRAM, Yücel TAŞTAN

Çocukluk çağının akut nekrotizan ensefalopatisi: Türkiye'den bir olgu

Çocukluk çağının akut nekrotizan ensefalopatisi, talamusta tipik, simetrik lezyonlarla, ak madde, beyin sapı ve serebellumun değişken tutulumuyla nitelenen, etiyolojisi bilinmeyen, nadir bir akut ensefalittir. Klinikte, gastrointestinal veya solunum sistemini etkileyen viral enfeksiyonlar sonrasında hızlı nörolojik bozulma izlenir. Asya kökenli çocuklarda daha sık görülür. Bu yazıda, bilinç bulanıklığı, ve ateş nedeniyle hastanemize başvuran, akut nekrotizan ensefalopati tanısı radyolojik bulgular ile konulan 3 yaşında bir erkek olgu sunuldu

Anahtar Kelimeler:

akut nekrotizan ensefalopati, çocukluk çağı, parainfluenza virus

Acute necrotizing encephalopathy of childhood: a Turkish case

Acute necrotizing encephalopathy of childhood (ANEC) is a rare form of acute encephalopathy of unknown etiology characterized by typical symmetrical lesions in the thalami, with variable involvement of the white matter, brainstem and cerebellum. Clinically there is a rapid neurologic deterioration after a short period of a nonspecific viral-like illness associated with gastrointestinal or respiratory signs. Asian children are especially affected. Here we present a 3-year-old boy admitted to our hospital with fever and deterioration of consciousness. The diagnosis of ANEC was made by radiologic findings

Keywords:

acute necrotizing encephalopathy, children, parainfluenza virus,

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Yazışma Adresi / Address for Correspondence: Dr. Olcay Ünver İstanbul University Cerrahpaşa Medical Scholl Department of Pediatric Neurology Tel: 0216 3910680 Fax: 0216 3910699
Email: olcaymd@hotmail.com. G eliş tarihi/Received on:15.11.2013
Kabul tarihi/Accepted on:26.12.2013